Arrhythmogenic Right Ventricular Cardiomyopathy Diagnosis

Authors

Amer Sayed, New York Medical College
Suman Pal, New York Medical College
Maria Poplawska, New York Medical College
Wilbert S. Aronow, New York Medical CollegeFollow
William H. Frishman, New York Medical CollegeFollow
Anthon Fuisz, New York Medical CollegeFollow
Jason T. Jacobson, New York Medical CollegeFollow

DOI

10.1097/CRD.0000000000000292

Journal Title

Cardiology in Review

First Page

319

Last Page

324

Document Type

Review Article

Publication Date

11-2020

Department

Medicine

Abstract

Arrhythmogenic right ventricular cardiomyopathy, formerly called "arrhythmogenic right ventricular dysplasia," is an under-recognized clinical entity characterized by ventricular arrhythmias and a characteristic ventricular pathology. Diagnosis is often difficult due to the nonspecific nature of the disease and the broad spectrum of phenotypic variations. Therefore, consensus diagnostic criteria have been developed which combine electrocardiographic, echocardiographic, cardiac magnetic resonance imaging and histologic criteria. In 1994, an international task force first proposed the major and minor diagnostic criteria of arrhythmogenic right ventricular cardiomyopathy based on family history, arrhythmias, electrocardiographic abnormalities, tissue characterization, and structural and functional right ventricular abnormalities. In 2010, the task force criteria were revised to include quantitative abnormalities. These diagnostic modalities and the most recent task force criteria are discussed in this review.

Recommended Citation

Sayed, A., Pal, S., Poplawska, M., Aronow, W. S., Frishman, W. H., Fuisz, A., & Jacobson, J. T. (2020). Arrhythmogenic Right Ventricular Cardiomyopathy Diagnosis. Cardiology in Review, 28 (6), 319-324. https://doi.org/10.1097/CRD.0000000000000292