A Rare Case Report of Malignant Peripheral Nerve Sheath Tumor Involving Both the Small Bowel and Large Bowel

Authors

Nazia Khan
Irma Hashmi
Liana Atallah
Hamid Shaaban, New York Medical CollegeFollow
Gunwant Guron, New York Medical CollegeFollow
Andre Fedida, New York Medical College

Author Type(s)

Faculty

DOI

10.4103/aam.aam_10_20

Journal Title

Annals of African Medicine

First Page

228

Last Page

231

Document Type

Case Report

Publication Date

7-1-2021

Department

Medicine

Abstract

Malignant peripheral nerve sheath tumor (MPNST) contains properties and histologic markers of both neural crest cells and mesenchymal cells. It is a rare diagnosis, with an incidence of 1:100,000/year or 4%-10% of soft-tissue sarcomas. There are very few cases reported and studied. Therefore, establishing a proper diagnosis and treatment of MPNST provides a challenge. We present this unique and rare case of metastatic MPNST of the small and large bowel with bone, pulmonary, liver, and splenic metastases. The patient subsequently developed hemorrhagic brain metastases and died 6 months after THE initial diagnosis.

Recommended Citation

Khan, N., Hashmi, I., Atallah, L., Shaaban, H., Guron, G., & Fedida, A. (2021). A Rare Case Report of Malignant Peripheral Nerve Sheath Tumor Involving Both the Small Bowel and Large Bowel. Annals of African Medicine, 20 (3), 228-231. https://doi.org/10.4103/aam.aam_10_20