NYMC Faculty Publications

Cor Triatriatum: A Review

Author Type(s)

Student, Faculty

DOI

10.1097/CRD.0000000000000626

Journal Title

Cardiology in Review

First Page

330

Last Page

333

Document Type

Article

Publication Date

7-1-2025

Department

Medicine

Keywords

atrial septal defect, congenital heart disease, cor triatriatum, cor triatriatum dexter, cor triatriatum sinister, echocardiogram, total anomalous pulmonary venous return

Disciplines

Medicine and Health Sciences

Abstract

Cor triatriatum is a rare congenital cardiac anomaly, characterized by a fibromuscular partition dividing the left (cor triatriatum sinister) or, rarely, the right atrium (cor triatriatum dexter). Occurring in 0.1-0.4% of congenital heart disease cases, it exhibits diverse clinical presentations, often mimicking mitral stenosis and left-sided heart failure, while occasionally remaining asymptomatic into adulthood. The embryological origin of cor triatriatum remains controversial. Recent years have seen the emergence of new classification systems that offer enhanced prognostic insights. Transthoracic echocardiography is the diagnostic cornerstone. Surgical resection, preferably under cardiopulmonary bypass, is the mainstay treatment, and is associated with favorable long-term outcomes.

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